Figures
Figure 1. Frontal and lateral radiography of the femur shows bilateral symmetric distal metadiaphyseal cortical thickening and diffuse medullary sclerosis with loss of corticomedullary differentiation.
Figure 2A-E. Fibrocollagenous stroma with clusters of foamy histiocytes (A); thickened bony trabeculae with features of cementum surrounding intertrabecular space filled with fibrous stroma (B) with variable proportion of foamy histiocytes (C). There is also infiltration of the foamy histiocytes accompanied by scattered lymphocytes within the soft tissue (adipose tissue at the right top corner) and rare multinucleated cells (arrow and inset) (D). Thickened trabeculae of laminar bone and its character under polarized light (inset) (E).
Figure 3A-C. Axial pre-contrast (A) and post-contrast (B) chest CT shows soft-tissue encasement of the aortic arch and descending thoracic aorta (coated aorta sign). On lung window (C) there are randomly distributed multiple different sized lung cysts with right lower lung ground glass opacities.
Figure 4A-D. Axial (A and B) contrast enhanced CT of abdomen shows ill-defined, plaque-like, heterogeneous soft tissue lesion infiltrating bilateral peri-renal spaces with thickening of anterior and posterior renal fascia ( hairy kidney sign) and no sign of hydronephrosis is seen. On the same images there is fat stranding of the mesentery. Coronal view (C and D) shows mild soft tissue encasement of the abdominal aorta and the proximal bilateral common iliac arteries (Coated aorta sign).